肺淋巴管肌瘤病利用影像学诊断的方法.doc

肺淋巴管肌瘤病利用影像学诊断的方法.doc肺淋巴管肌瘤病利用影像学诊断的方法
要】目的探讨肺淋巴管肌瘤病的影像学特征,提高对该病的诊断水平。方法回顾性分析我院确诊的肺淋巴管肌瘤病11例,全部病例均行胸部x线检查及胸部hrct检查。结果胸部x线表现无明显特异性。hrct的特征性表现为双肺弥漫分布的圆形或多边形囊腔,囊腔直径2-40mm左右,大多数小于10mm,囊壁厚度小于1mm。结论肺淋巴管肌瘤病是一种罕见病,其影像学表现具有特征性,影像学检查尤以hrct检查对该病的诊断具有重要的意义。
【关键词】肺淋巴管肌瘤病;体层摄
image features of pulmonary lymphangioleiomyomatosis
fan qi-yun, sang ling, zeng qing-shi.
department of image, the first affiliated hospital of guangzhou medical college. guangzhou, 510120, china
[abstract] objective to investigate image features of pulmonary lymphangioleiomyomatosis(plam) and to improve its diagnosis. methods eleven patients underage features anifestation, the characteristic hrct manifestation ultiple, different sized cystoid transparent areas,ost cysts m in diameter(2-40mm),the cysts cliff m. conclusion plam is a rare disease, image examinations have characteristic signs especially hrct
[key onary lymphangioleiomyomatosis; tomography, x-ray puted; high resolution ct
肺淋巴管肌瘤病(pulmonary lymphangioleiomyomatosis)是一种罕见的,病因不明的持续发展的肺间质疾病,主要发生在育龄期妇女。.,现予以报道,并就其影像学特征及胸片与hrct对该病的诊断价值进行探讨。
材料与方法
11例均为女性,年龄20-49岁,平均30岁。临床症状中呼吸困难占91%,气胸73%,疲乏占72%,乳糜胸水占36%,咳嗽占36%,胸痛占27%,咳血占27%。全部病例均有胸片检查及hrct检查,ct机为toshiba 16排螺旋ct机,层厚2mm,层距2mm,扫描方位由胸廓入口处到横膈水平。11例中8例由纤维支气管镜肺活检证实,3例由开胸肺活检证实。
结果

11例患者中4例出现双肺X格状阴影伴液气胸,4例单纯出现气胸,3例表现为双肺肺纹理增粗紊乱,呈小X格状改变,均无明显特异性。

双肺广泛分布的弥漫性小囊状改变,分布较均匀。囊腔类圆形,直径2-40mm左