14-Crow-Fukase综合征44例临床分析.pdf

《中国医学前沿杂志(电子版)》2012年第4卷第10期●百家病例讨论● 71
第021例 Crow-Fukase综合征44例临床分析
孙斌1,马烈2,郎森阳3,蒲传强3,于生元3(,廊坊 065201;
东省东莞康华医院神经内科,东莞 523080;,北京 100853)
【摘要】目的对我们诊治的44例Crow-Fukase综合征患者资料与国外的报道组进行对比分析,探索
中国患者的特点,以提高临床诊治水平。方法将44例(包括解放军总医院35例,其他医院9例)
Crow-Fukase综合征患者资料与国外报道的临床资料进行列表对比。结果发现各组周围神经病发生率
100%,而本组的脾肿大,胸、腹水发生率高于国外组;女性化乳房、M-蛋白、厚糙皮发生率低于国
外组。结论 Crow-Fukase综合征可见多系统损害,国内外各组病例表现类似,其病因与免疫系统的异
常有关。
【关键词】Crow-Fukase综合征;多系统损害;临床;治疗
44 cases reports of Crow-Fukase syndrome
SUN Bin1, MA Lie2, LANG Sen-yang3, PU Chuan-qiang3, YU Sheng-yuan3( Centre of Neurological
diseases, YanDa International Hospital, Langfang 065201, China; of Neurology, KangHua
Hospital of Guangdong, Dongguan 523080, China; of Neurology, General Hospital of PLA,
Beijing 100853, China)
Corresponding author:SUN Bin, Email:sunbin301@
【Abstract】Objective We make a diagnosis and give treatment to 44 cases of Crow-Fukase syndrome and
foreign groups contrast analysis, explored the characteristics of Chinese patients, in order to improve the
clinical treatment level. Methods 44 cases data (including 35 cases from general hospital of PLA, and 9 cases
from other hospitals) and foreign coverage clinical data contrast list. Results It was found that the periphery
neurolopathy as 100% in every group, and the spleen enlargeme