风湿性疾病相关综合征.pptx

风湿性疾病相关综合征
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A summary of syndromes (1)
Felty syndrome
Reiter’s Syndrome (Reactive Arthritis)
PONCET syndrome
CREST syndrome
Churg-Strauss syndrome
Hemophagocytic syndrome
Macrophage Activation Syndrome
SAPHO syndrome
Paraneoplastic rheumatologic syndrome
POEMS syndrome
Ehlers-Danlos syndrome
Weber-Christian syndrome
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A summary of syndromes (2)
Sjogren’s syndrome
Antiphospholipid syndrome (APS)
Bechet’s syndrome
RS3PE syndrome
Overlap syndrome
Raynaud’s syndrome
Undifferentiated polyarthritis syndrome
Lupus anticoagulant hypoprothrombinemia syndrome (LAHS)
Rowell’s syndrome
Drug-induced lupus syndromes
Cogan’s syndrome
Large granular lymphocyte syndrome
Caplan’s syndrome
Palindromic syndrome
Shrinking lung syndrome
Thrombotic thrombocytopenic purpura–hemolytic uremic syndrome (TTP-HUS)
Neuropsychiatric lupus (NPSLE) syndrome
Lambert-Eaton myasthenic syndrome (LEMS)
Sweet’s syndrome
Chronic Infantile Neurologic Cutaneous and Articular (CINCA) Syndrome
Parry-Romberg syndrome
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Other syndromes
Löfgren’s syndrome
Hemolytic uremic syndrome
HELLP (hemolysis, elevated liver enzymes, low platelets) syndrome
Waterhouse-Friderichsen syndrome (WFS)
Carpal tunnel syndrome
Milwaukee shoulder syndrome
Greater trochanteric pain syndrome
Femoroacetabular impingement syndrome
Demyelinating syndromes
Frank nephrotic syndrome
Cold agglutinin syndrome
Hyperviscosity syndrome
Stiff skin syndrome
Werner’s syndrome
Shulman’s syndrome or fasciitis-panniculitis syndrome
Carcinoid syndrome
Eosinophilia-myalgia syndrome
Chronic fatigue syndrome
Toxic oil syndrome
Parry-Romberg syndrome
Hypocomplementemic urticarial vasculitis syndrome
Hypereosinophilic syndrome
Papular-purpuric gloves and socks syndrome (PPGSS)
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Felty’s syndrome
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Felty首先提出，用于描述慢性关节炎、脾大、粒细胞减少三联征
见于血清阳性侵蚀性强的RA，为RA患者罕见的症状群，在美国RA患者中发生的概率约为1-3%
RA患者出现FS提示关节炎及关节外表现严重、预后差
Felty’s syndrome (FS)：定义
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Felty’s syndrome (FS)：诊断
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